Giant bilateral fibrous dysplasia of first ribs: compression of mediastinum and thoracic outlet.

نویسندگان

  • V Thomas de Montpréville
  • E Dulmet
  • R Ponlot
  • P Dartevelle
چکیده

A 43 year old woman presented with two large bilateral tumours of the first ribs that compressed the right subclavian vessels, trachea and oesophagus and led to right arm oedema, severe dyspnoea and dysphagia. The resected tumours showed typical histological features of fibrous dysplasia without malignant transformation. The right tumour weighed 1.5 kg and measured 17 x 13 x 10 cm. This report demonstrates that major surgery is still possible for resection of such exceptional giant compressive lesions, since fibrous dysplasia is a benign and non-infiltrative tumour.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Evaluation of Neurovascular Complication of Cervical Ribs

Introduction: Cervical rib is relatively uncommon congenital abnormality that originates from the seventh cervical vertebrae and rarely from the sixth vertebrae. The purpose of this paper is to consider that this abnormal condition is an important cause of neurovascular compression at the thoracic outlet. Methods: In this study all patients who were referred to radiology departm...

متن کامل

Giant fibrous dysplasia arising from ribs.

A 46-year-old male patient with swelling and pain in the right chest wall was admitted to our clinic. The lesion originating from the second, third and fourth ribs was resected en bloc via right thoracotomy (Figs 1 and 2). The defect was closed using-prolene mesh. Pathological examination revealed a fibrous dysplasia. Figure 1: Axial and coronal CT images showing the lesion originating from the...

متن کامل

Treatment of Polyostotic Fibrous Dysplasia of the Thoracic Spine with Intravenous Pamidronate: Result from 9 Months Follow Up

Fibrous dysplasia of the spine is very rarely observed. We reported a case of a 57-year-old woman, who presented with neck and bilateral shoulder pain with histologically confirmed fibrous dysplasia, involving the first and second thoracic vertebrae. Clinical and radiological findings were not specific for fibrous dysplasia. The histological biopsy was required for a confirmed diagnosis. Endocr...

متن کامل

Rib Abnormalities Investigated by Computed Tomography: A Report on Common and Uncommon Cases

Purpose: Rib anomalies include numerical and structural categories. This study investigates the costal abnormalities by computed tomography scan in an Iranian population. Methods: In a retrospective study, 400 Chest CT scans (225 (56.2%) male, and 175 (43.8%) female) aging from 18 to 89 were investigated for one year (2020 to 2021). Images were carefully observed and various abnormalities suc...

متن کامل

Thoracic outlet syndrome.

Diagnosis and treatment of thoracic outlet syndrome (TOS) involves neurologists, physiatrists, family physicians, orthopedic surgeons, vascular surgeons, thoracic surgeons, neurosurgeons and sometimes psychiatrists. It is generally accepted that TOS is caused by compression of brachial plexus elements or subclavian vessels in their passage from the cervical area toward the axilla and proximal a...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • The European respiratory journal

دوره 8 6  شماره 

صفحات  -

تاریخ انتشار 1995